Cystic fibrosis is a disorder that causes severe lung damage and nutritional deficiencies. This life-threatening disorder is a genetic condition that causes individuals with CF to produce thick and sticky mucus secretions. Cells that produce mucus, saliva, sweat and digestive juices are greatly affected. Mucus that normally acts as a lubricant can block airways and passageways in the lungs and pancreas. Respiratory failure is a common problem with CF. CF sometimes requires lung transplantation as well as other surgeries to correct complications associated with CF.
There are many treatments available for CF and its symptoms. The main complications are infection, too much mucus, decreased airflow, malnutrition and other complications resulting from poor digestion. Treatments include:
Keep immunizations up to date; this includes influenza and pneumonia vaccinations as suggested by your doctor. These will help keep infections down.
Children with CF will need to have the mucus physically removed from their lungs. This is done with chest percussions by manually clapping on the chest from the front and back. This is best done with their head leaning downward to allow the gravity to help clear the secretions. Sometimes an electric or mechanical percussor is used. An inflatable vest that vibrates with high frequency can also be used to help your child or infant cough up secretions. Infants and children need daily percussions done at least twice a day. Our respiratory therapist can show you the best way to do this.
Exercise is important for people with CF. Activity and exercise helps to loosen the mucus in the lungs and causes the child to cough more. It also strengthens the heart and muscles needed to breathe. Make sure your child is given a nutritious diet and follow the advice of your doctor or dietician. CF can cause children to become malnourished because normal enzymes cannot reach the intestines. Pancreatic enzymes and vitamins can help your child absorb nutrients and stay at a healthy weight. Medical Equipment for Cystic Fibrosis RSVP Home Care is equipped with all the equipment you will need to care for your infant or child with CF. This includes mechanical percussors and vests as well as other respiratory and post surgical needs. Our professional respiratory therapists are able to offer you the home care you need as well. Having a licensed respiratory therapist on your home health care team can give you the confidence and assurance that you desire when you’re caring for your child at home.
Ventilators – LTV 950 and 1150 Trilogy
Ventilator supplies; circuits, humidifiers
Aerosol compressors (50 PSI) & supplies
Nebulizers & supplies
Suction machines & supplies (oral and tracheal)
Trach. Tubes (Shiley, Bivona, Smiths) standard & custom sizes
High pressure systems
Oximeters and Probes
Enteral pumps & poles
Nutrients & feeding kits
G-tubes, N/G tubes & supplies
MIC-KEY buttons & supplies
Complete line of dressings & gauze supplies
Incontinent supplies & Uri logical supplies